RARE COEXISTENCE OF MITRAL AND PULMONARY ATRESIA WITH DOUBLE OUTLET RIGHT VENTRICLE. CASE REPORT AND REVIEW OF LITERATURE

Akhil Mehrotra*, Mohammad Shaban and Faiz Illahi Siddiqui

Double-outlet right ventricle (DORV) represents a rare group of cardiac anomalies characterized by both great arteries arising primarily from the RV. This disease is a conotruncal anomaly as a complex heart disease and comprises less than 1% of all congenital heart anomalies. The first diagnostic criterion for DORV is the rise of both the aorta and the pulmonary artery from the morphologic RV. Other cardiac malformations are always present with the frequent coexistence of multiple abnormalities. These may include 1 or more ventricular septal defects, left ventricular outflow obstruction, and atrioventricular valve abnormalities. DORV may occur with any atrial situs and many other variations; nonetheless, situs solitus and atrioventricular concordance are the most common findings. We herein present an extremely rare case of 13 day old neonatal male suffering from DORV alongwith mitral and pulmonary atresia.